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Iridocorneal Endothelial (ICE) Syndrome, Cogan-Reese/Iris Nevus Syndrome Subtype with Secondary Angle Closure Glaucoma A patient presented with a 3-day history of unilateral worsening eye pain, blurry vision and irregular pupil in the right eye. Found to have elevated IOP at an outside facility and…

Iris Pigment Epithelial Cysts A patient with a history of amblyopia and coloboma presented with decreased vision in both eyes over the past 2 years. Slit lamp exam was notable for pigmented lesions prolapsing through pupil and adhering to posterior cornea in both eyes. The patient sought surgical i…

IRVAN (Idiopathic Retinal Vasculitis, Aneurysms, and Neuroretinitis) A patient presented to the BPEI Emergency Room with a red painful eye and blurred vision. At the time of presentation she was diagnosed with elevated intraocular pressure in the setting of neovascularization of the optic nerve, ir…

IRVAN Syndrome An adult patient presented to the Uveitis clinic for evaluation after developing visual deficits in the right eye. He was previously diagnosed with multiple branch retinal artery and vein occlusions in both eyes concerning for an occlusive retinal vasculitis. On examination he was fo…

Isolated Spherophakia A patient with ocular hypertension and narrow angle was found to have Isolated Spherophakia. She underwent phacoemulsification with a capsular tension ring and intraocular lens in the bag OS. She then had a pars plana vitrectomy with a scleral fixated lens OD. Post-operatively…

Juvenile Myasthenia Gravis A child previously healthy, presented to the ED with his mother for new onset right upper eyelid ptosis of few weeks duration. History was significant for variability in eye alignment over the past few months. Exam was notable for right upper eyelid ptosis with MRD1 of -2…

Juvenile Psammomatous Ossifying Fibroma An 18-year-old female presented with blurry vision, headaches for 4 months. She was diagnosed to have papilledema on an outside eye exam and referred to BPEI. Her visual acuity was 20/20 OD, 20/100 OS. Additionally, she was noted to have junctional scotoma on…

Juvenile X-linked Retinoschisis A pediatric patient with a past medical history of Kawasaki disease presents for retinal evaluation of reported vitreous hemorrhage in the right eye and retinal detachment in the left eye. The visual acuity was 20/200 in the right eye and 20/800 in the left eye. The …

Juvenile Xanthogranuloma Patient presented to the BPEI emergency room with tearing and light sensitivity of the right eye for 1 month. Examination revealed grimace-to-light vision, soft to palpation intraocular pressure, and hyphema. Skin examination revealed yellowish raised skin lesions on the ne…

Juvenile Xanthogranuloma A baby was referred for a new-onset subconjunctival lesion in the right eye. He was found to have a thickened, yellow corneoscleral lesion and hyphema, presumed to be ocular juvenile xanthogranuloma (JXG). He was started on topical steroids as empiric treatment, with initia…

Kaposi's Sarcoma of the Conjunctiva A patient presented to the BPEI Emergency Room with a painless red eye for the past 3 months. Past medical history was limited to a recent hospitalization for a complicated pneumonia and a new diagnosis of HIV. Examination of the eye revealed an elevated, vascula…

Keratitis Due to Severe Sinonasal Disease with Underlying Granulomatosis with Polyangiitis A young patient with no known prior medical history presents with decreased vision and pain in the right eye. On presentation, patient’s exam was notable for visual acuity of 20/150 in the right eye and 20/…

Klebsiella Pneumoniae Endogenous Endophthalmitis A 46-year-old healthy male presented with a red and painful eye with a preceding febrile gastrointestinal illness. Examination and work-up revealed concomitant intraocular and liver abscesses that required pars plana vitrectomy, drainage of subretina…

Knobloch Syndrome An infant presented to the eye clinic with nystagmus. The patient underwent examination. Initial eye examination revealed horizontal nystagmus, a midline occipital scalp lesion, hypoplastic macula in both eyes, and high myopia (greater than -15.0 D in both eyes). Given a family hi…

Lattice Corneal Dystrophy Lattice corneal dystrophy is a rare disease with a variety of etiologies. Historically, corneal dystrophies have been defined as bilateral, progressive processes that start in a patient’s first to second decade of life and have no correlation with systemic illnesses. Whi…

Leber Hereditary Optic Neuropathy – LHON An 18-year-old healthy man was evaluated in the eye emergency room for acute progressive painless vision loss in both eyes. First was affected a right eye and a six days later, left eye was affected too. Best-corrected visual acuity was 20/800 right eye an…

Leber Hereditary Optic Neuropathy An 18-year-old male presented to the ER with bilateral decreased vision and eye pain for 10 days. His visual acuity was HM OD, 20/300 OS. He was noted to have disc pallor OD and temporal pallor with slight nasal elevation OS on fundus exam. His MRI showed T2 hyper …

Leber Hereditary Optic Neuropathy (LHON) A previously healthy patient presented to the emergency department (ED) with a 2-week history of bilateral blurry vision associated with painful eye movement. The patient denied eye redness, eye discharge, photophobia, double vision, or headache. The ophthal…

Leber's Hereditary Optic Neuropathy A patient came to ED due to subacute decreased vision in his right eye since 1/2023. He had a history of decreased vision in his left eye following phacoemulsification surgery in Oct 2022. BCVA was 20/70 OD and 20/400 OS Past medical history was positive for HTN,…

Leukemic Optic Neuropathy Leukemic optic neuropathy is a rare entity that is characterized as optic nerve dysfunction resulting from direct infiltration of neoplastic leukocytes. It is an indicator of central nervous system involvement, and it is a neuro-ophthalmic and oncologic emergency that warr…