A 50-year-old female with previous history of sickle cell disease of unknown type presented with a vitreous hemorrhage in the left eye. Subsequent follow up revealed Stage 3 proliferative sickle cell retinopathy (PSR) in the right eye and Stage 5 PSR in the left eye with an associated mixed tractional and rhegmatogenous retinal detachment. The latter was repaired via combined scleral buckling-pars plana vitrectomy and silicone oil tamponade and vision improved from HM to 20/200. The patient deferred any treatment for her right eye. Eighteen months after initial presentation, her right eye had progressed to Stage 5 PSR with mixed tractional and rhegmatogenous retinal detachment, which was repaired with combined buckling-vitrectomy and silicone oil tamponade. Six weeks after surgery, her retina remained attached and vision had improved from 20/400 to 20/50. Hemoglobin analysis revealed Hb SC phenotype.
Presentation Date: 10/31/2019
Issue Date: 08/01/2020